KLASYFIKACJA WHO GUZÓW OUN 2007 (WHO CLASSIFICATION OF THE TUMORS OF THE CNS 2007)
  1. Tumours of neuroepithelial tissue

    1. Astrocytic tumours

      1. Pilocytic astrocytoma (ICD-O 9421/1, WHO grade I)

      2. Pilomyxoid astrocytoma (ICD-O 9425/3, WHO grade II)

      3. Subependymal giant cell astrocytoma (ICD-O 9384/1, WHO grade I)

      4. Pleomorphic xanthoastrocytoma (ICD-O 9424/3, WHO grade II)

      5. Diffuse astrocytoma (ICD-O 9400/3, WHO grade II)

        1. Fibrillary astrocytoma (ICD-O 9420/3, WHO grade II)

        2. Gemistocytic astrocytoma (ICD-O 9411/3, WHO grade II)

        3. Protoplasmic astrocytoma (ICD-O 9410/3, WHO grade II)

      6. Anaplastic astrocytoma (ICD-O 9401/3, WHO grade III)

      7. Glioblastoma (ICD-O 9440/3, WHO grade IV)

        1. Giant cell glioblastoma (ICD-O 9441/3, WHO grade IV)

        2. Gliosarcoma (ICD-O 9442/3, WHO grade IV)

      8. Gliomatosis cerebri (ICD-O 9381/3, WHO grade III)

    2. Oligodendroglial tumours

      1. Oligodendroglioma (ICD-O 9450/3, WHO grade II)

      2. Anaplastic oligodendroglioma (ICD-O 9451/3, WHO grade III)

    3. Oligoastrocytic tumours

      1. Oligoastrocytoma (ICD-O 9382/3, WHO grade II)

      2. Anaplastic oligoastrocytoma (ICD-O 9382/3, WHO grade III)

    4. Ependymal tumours

      1. Subependymoma (ICD-O 9383/1, WHO grade I)

      2. Myxopapillary ependymoma (ICD-O 9394/1, WHO grade I)

      3. Ependymoma (ICD-O 9391/3, WHO grade II)

        1. Cellular (ICD-O 9391/3, WHO grade II)

        2. Papillary (ICD-O 9393/3, WHO grade II)

        3. Clear cell (ICD-O 9391/3, WHO grade II)

        4. Tanycytic (ICD-O 9391/3, WHO grade II)

      4. Anaplastic ependymoma (ICD-O 9392/3, WHO grade III)

    5. Choroid plexus tumours

      1. Choroid plexus papilloma (ICD-O 9390/0, WHO grade I)

      2. Atypical choroid plexus papilloma ( ICD-O 9390/1, WHO grade II)

      3. Choroid plexus carcinoma (ICD-O 9390/3, WHO grade III)

    6. Other neuroepithelial tumours

      1. Astroblastoma (ICD-O 9430/3, WHO grade I)

      2. Chordoid glioma of the third ventricle (ICD-O 9444/1, WHO grade II)

      3. Angiocentric glioma (ICD-O 9431/1, WHO grade I)

    7. Neuronal and mixed neuronal-glial tumours

      1. Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos) (ICD-O 9493/0)

      2. Desmoplastic infantile astrocytoma/ganglioglioma (ICD-O 9412/1, WHO grade I)

      3. Dysembryoplastic neuroepithelial tumour (ICD-O 9413/0, WHO grade I)

      4. Gangliocytoma (ICD-O 9492/0, WHO grade I)

      5. Ganglioglioma (ICD-O 9505/1, WHO grade I)

      6. Anaplastic ganglioglioma (ICD-O 9505/3, WHO grade III)

      7. Central neurocytoma (ICD-O 9506/1, WHO grade II)

      8. Extraventricular neurocytoma (ICD-O 9506/1, WHO grade II)

      9. Cerebellar liponeurocytoma (ICD-O 9506/1, WHO grade II)

      10. Papillary glioneuronal tumour (ICD-O 9509/1, WHO grade I)

      11. Rosette-forming glioneuronal tumour of the fourth ventricle (ICD-O 9509/1, WHO grade I)

      12. Paraganglioma (ICD-O 8680/1, WHO grade I)

    8. Tumours of the pineal region

      1. Pineocytoma (ICD-O 9361/1, WHO grade I)

      2. Pineal parenchymal tumour of intermediate differentiation (ICD-O 9362/3, WHO grade II, III)

      3. Pineoblastoma (ICD-O 9362/3, WHO grade IV)

      4. Papillary tumors of the pineal region (ICD-O 9395/3, WHO grade II, III)

    9. Embryonal tumours

      1. Medulloblastoma (ICD-O 9470/3, WHO grade IV)

        1. Medulloblastoma with extensive nodularity (ICD-O 9471/3, WHO grade IV)

        2. Anaplastic medulloblastoma (ICD-O 9474/3, WHO grade IV)

        3. Large cell medulloblastoma ((ICD-O 9474/3, WHO grade IV)

      2. CNS Primitive neuroectodermal tumour (ICD-O 9473/3, WHO grade IV)

        1. CNS Neuroblastoma (ICD-O 9500/3, WHO grade IV)

        2. CNS Ganglioneuroblastoma (ICD-O 9490/3, WHO grade IV)

        3. Ependymoblastoma (ICD-O 9392/3, WHO grade IV)

      3. Atypical teratoid/rhabdoid tumour (ICD-O 9508/3, WHO grade IV)

  2. Tumours of cranial and paraspinal nerves

    1. Schwannoma (IDC-O 9560/0, WHO grade I)

    2. Neurofibroma (IDC-O 9540/0, WHO grade I)

    3. Perineurioma (IDC-O 9571/0, 9571/3, WHO grade I, II, III)

    4. Malignant peripheral nerve sheath tumour (MPNST) (IDC-O 9540/3, WHO grade II, III, IV)

  3. Tumours of the meninges

    1. Tumours of meningothelial cells

      1. Meningioma (IDC-O 9530/0, WHO grade I)

        1. Meningothelial (IDC-O 9531/0, WHO grade I)

        2. Fibrous (IDC-O 9532/0, WHO grade I)

        3. Transitional (IDC-O 9537/0, WHO grade I)

        4. Psammomatous (IDC-O 9533/0, WHO grade I)

        5. Angiomatous (IDC-O 9534/0, WHO grade I)

        6. Microcystic (IDC-O 9530/0, WHO grade I)

        7. Secretory (IDC-O 9530/0, WHO grade I)

        8. Metaplastic (IDC-O 9530/0, WHO grade I)

        9. Chordoid (IDC-O 9538/1)

        10. Clear cell (IDC-O 9538/1)

        11. Papillary (IDC-O 9538/3)

        12. Rhabdoid (IDC-O 9538/3)

        13. Atypical meningioma (IDC-O 9539/1, WHO grade II)

        14. Anaplastic meningioma (IDC-O 9530/3, WHO grade III)

    2. Mesenchymal tumours

      1. Lipoma (IDC-O 8850/0)

      2. Angiolipoma (IDC-O 8861/0)

      3. Hibernoma (IDC-O 8880/0)

      4. Liposarcoma (IDC-O 8850/3)

      5. Solitary fibrous tumour (IDC-O 8815/0)

      6. Fibrosarcoma (IDC-O 8810/3)

      7. Malignant fibrous histiocytoma (IDC-O 8830/3)

      8. Leiomyoma (IDC-O 8890/0)

      9. Leiomyosarcoma (IDC-O 8890/3)

      10. Rhabdomyoma (IDC-O 8900/0)

      11. Rhabdomyosarcoma (IDC-O 8900/3)

      12. Chondroma (IDC-O 9220/0)

      13. Chondrosarcoma (IDC-O 9220/3)

      14. Osteoma (IDC-O 9180/0)

      15. Osteosarcoma (IDC-O 9180/3)

      16. Osteochondroma (IDC-O 9210/0)

      17. Haemangioma (IDC-O 9120/0)

      18. Epithelioid hemangioendothelioma (IDC-O 9133/1)

      19. Haemangiopericytoma (IDC-O 9150/1, WHO grade II)

      20. Anaplastic haemangiopericytoma (IDC-O 9150/3, WHO grade III)

      21. Angiosarcoma (IDC-O 9120/3)

      22. Kaposi sarcoma (IDC-O 9140/3)

      23. Ewing sarcoma - PNET (IDC-O 9364/3)

    3. Primary melanocytic lesions

      1. Diffuse melanocytosis (IDC-O 8728/0)

      2. Melanocytoma (IDC-O 8728/1)

      3. Malignant melanoma (IDC-O 8720/3)

      4. Meningeal melanomatosis (IDC-O 8728/3)

    4. Other neoplasms related to the meninges

      1. Haemangioblastoma (IDC-O 9161/1, WHO grade I)

  4. Tumors of the haematopoietic system

    1. Malignant lymphomas (IDC-O 9590/3)

    2. Plasmocytoma (IDC-O 9731/3)

    3. Granulocytic sarcoma (IDC-O 9930/3)

  5. Germ cell tumours

    1. Germinoma (IDC-O 9064/3)

    2. Embryonal carcinoma (IDC-O 9070/3)

    3. Yolk sac tumour (IDC-O 9071/3)

    4. Choriocarcinoma (IDC-O 9100/3)

    5. Teratoma (IDC-O 9080/1)

    6. Mixed germ cell tumours (IDC-O 9085/3)

  6. Tumours of the sellar region

    1. Craniopharyngioma (IDC-O 9350/1, WHO grade I)

      1. Adamantinomatous (IDC-O 9351/1, WHO grade I)

      2. Papillary (IDC-O 9352/1, WHO grade I)

    2. Granular cell tumour (IDC-O 9582/0, WHO grade I)

    3. Pituicytoma (IDC-O 9432/1, WHO grade I)

    4. Spindle cell oncocytoma of the adenohypophysis (IDC-O 8991/0, WHO grade I)

  7. Metastatic Tumours

 

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